alpha-L-Iduronidase / Unconjugated /

Product Details
Supplier Biorbyt
Catalog #: orb100057-200ug (View supplier product page)
Size 200 μg
Price $610.30
Antigen alpha-L-Iduronidase
Clone
Host Rabbit
Isotype IgG
Conjugate Unconjugated
Target Species Human, Mouse, Rat
Applications WB, IHC-P, IF, ELISA
Description Rabbit Polyclonal to MPS1.
About alpha-L-Iduronidase and Purified
alpha-L-Iduronidase This gene encodes an enzyme that hydrolyzes the terminal alpha-L-iduronic acid residues of two glycosaminoglycans, dermatan sulfate and heparan sulfate. This hydrolysis is required for the lysosomal degradation of these glycosaminoglycans. Mutations in this gene that result in enzymatic deficiency lead to the autosomal recessive disease mucopolysaccharidosis type I (MPS I). [provided by RefSeq, Jul 2008]
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Purified Excitation and Emission Spectra