alpha Galactosidase / Unconjugated /

Product Details
Supplier Sino Biological
Catalog #: 50964-RP01 (View supplier product page)
Size 100 μl
Price $99.00
Antigen alpha Galactosidase
Clone
Host Rabbit
Isotype IgG
Conjugate Unconjugated
Target Species Mouse
Applications ELISA
Description Produced in rabbits immunized with purified, recombinant Mouse GLA / Alpha-galactosidase A (rM GLA / Alpha-galactosidase A; Catalog#50964-M08H; Q8BGZ6; Met1-Arg421). Total IgG was purified by Protein A affinity chromatography.
About alpha Galactosidase and Purified
alpha Galactosidase This gene encodes a homodimeric glycoprotein that hydrolyses the terminal alpha-galactosyl moieties from glycolipids and glycoproteins. This enzyme predominantly hydrolyzes ceramide trihexoside, and it can catalyze the hydrolysis of melibiose into galactose and glucose. A variety of mutations in this gene affect the synthesis, processing, and stability of this enzyme, which causes Fabry disease, a rare lysosomal storage disorder that results from a failure to catabolize alpha-D-galactosyl glycolipid moieties. [provided by RefSeq, Jul 2008]
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Purified Excitation and Emission Spectra