CPS1 / Unconjugated /

Product Details
Supplier Boster Biological Technology
Catalog #: M01320-1 (View supplier product page)
Size 100 μg
Price $299.00
Antigen CPS1
Clone
Host Rabbit
Isotype IgG
Conjugate Unconjugated
Target Species Human, Mouse, Rat
Applications IP, IF, IHC, WB
Description Rabbit IgG Monoclonal antibody for P31327 detection. Tested positive for WB IHC IF/IF IP in Human Mouse Rat
About CPS1 and Purified
CPS1 The mitochondrial enzyme encoded by this gene catalyzes synthesis of carbamoyl phosphate from ammonia and bicarbonate. This reaction is the first committed step of the urea cycle, which is important in the removal of excess urea from cells. The encoded protein may also represent a core mitochondrial nucleoid protein. Three transcript variants encoding different isoforms have been found for this gene. The shortest isoform may not be localized to the mitochondrion. Mutations in this gene have been associated with carbamoyl phosphate synthetase deficiency, susceptibility to persistent pulmonary hypertension, and susceptibility to venoocclusive disease after bone marrow transplantation.[provided by RefSeq, May 2010]
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