alpha-L-Iduronidase Monoclonal / Unconjugated / 452619
alpha-L-Iduronidase Monoclonal / Unconjugated / 452619
Product Details
Supplier | R&D Systems | |
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Catalog #: | MAB4119 (View supplier product page) | |
Size | 100 μg | |
Price | $469.00 | |
Antigen | alpha-L-Iduronidase | |
Clone | 452619 | |
Host | Mouse | |
Isotype | IgG1 | |
Conjugate | Unconjugated | |
Target Species | Human | |
Applications | WB | |
Description | Human alpha -L-Iduronidase/IDUA Antibody |
About alpha-L-Iduronidase and Purified
alpha-L-Iduronidase | This gene encodes an enzyme that hydrolyzes the terminal alpha-L-iduronic acid residues of two glycosaminoglycans, dermatan sulfate and heparan sulfate. This hydrolysis is required for the lysosomal degradation of these glycosaminoglycans. Mutations in this gene that result in enzymatic deficiency lead to the autosomal recessive disease mucopolysaccharidosis type I (MPS I). [provided by RefSeq, Jul 2008] |
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Citations
Reviews & Ratings
Purified Excitation and Emission Spectra
$469.00
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