alpha-L-Iduronidase / Unconjugated / Polyclonal

Product Details
Supplier Bio-Rad
Catalog #: VPA00140K (View supplier product page)
Size 10 Westerns
Price $330.00
Antigen alpha-L-Iduronidase
Clone Polyclonal
Host Goat
Isotype IgG
Conjugate Unconjugated
Target Species Human
Applications WB
Description MPS1 ANTIBODY WITH CONTROL LYSATE
About alpha-L-Iduronidase and Purified
alpha-L-Iduronidase This gene encodes an enzyme that hydrolyzes the terminal alpha-L-iduronic acid residues of two glycosaminoglycans, dermatan sulfate and heparan sulfate. This hydrolysis is required for the lysosomal degradation of these glycosaminoglycans. Mutations in this gene that result in enzymatic deficiency lead to the autosomal recessive disease mucopolysaccharidosis type I (MPS I). [provided by RefSeq, Jul 2008]
Citations
Additional
Sources
Reviews & Ratings
Submit a Review

Purified Excitation and Emission Spectra