alpha Galactosidase / Unconjugated / 23GB5545

Product Details
Supplier Thermo Fisher Scientific
Catalog #: MA5-53897 (View supplier product page)
Size 20 µL
Price $199.00
Antigen alpha Galactosidase
Clone 23GB5545
Host Rabbit
Isotype IgG
Conjugate Unconjugated
Target Species Human
Applications FC, WB
Description alpha Galactosidase Recombinant Rabbit Monoclonal Antibody (23GB5545)
About alpha Galactosidase and Purified
alpha Galactosidase This gene encodes a homodimeric glycoprotein that hydrolyses the terminal alpha-galactosyl moieties from glycolipids and glycoproteins. This enzyme predominantly hydrolyzes ceramide trihexoside, and it can catalyze the hydrolysis of melibiose into galactose and glucose. A variety of mutations in this gene affect the synthesis, processing, and stability of this enzyme, which causes Fabry disease, a rare lysosomal storage disorder that results from a failure to catabolize alpha-D-galactosyl glycolipid moieties. [provided by RefSeq, Jul 2008]
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Purified Excitation and Emission Spectra