alpha Galactosidase / Unconjugated / Gal13
alpha Galactosidase / Unconjugated / Gal13
Product Details
Supplier | Absolute Antibody | |
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Catalog #: | Ab01163-1.1-unconjugated (View supplier product page) | |
Size | 200 μg | |
Price | ||
Antigen | alpha Galactosidase | |
Clone | Gal13 | |
Host | Mouse | |
Isotype | IgG1 | |
Conjugate | Unconjugated | |
Target Species | Bovine, Rabbit | |
Applications | ELISA | |
Description | Anti-alpha-Gal [Gal13] |
About alpha Galactosidase and Purified
alpha Galactosidase | This gene encodes a homodimeric glycoprotein that hydrolyses the terminal alpha-galactosyl moieties from glycolipids and glycoproteins. This enzyme predominantly hydrolyzes ceramide trihexoside, and it can catalyze the hydrolysis of melibiose into galactose and glucose. A variety of mutations in this gene affect the synthesis, processing, and stability of this enzyme, which causes Fabry disease, a rare lysosomal storage disorder that results from a failure to catabolize alpha-D-galactosyl glycolipid moieties. [provided by RefSeq, Jul 2008] |
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