alpha Galactosidase / Unconjugated / Gal13

Product Details
Supplier Absolute Antibody
Catalog #: AB01163-23.0-200UG (View supplier product page)
Size 200 μg
Price $555.00
Antigen alpha Galactosidase
Clone Gal13
Host Rabbit
Isotype IgG
Conjugate Unconjugated
Target Species Bovine, Rabbit
Applications ELISA
Description Anti alpha-Gal [Gal13]
About alpha Galactosidase and Purified
alpha Galactosidase This gene encodes a homodimeric glycoprotein that hydrolyses the terminal alpha-galactosyl moieties from glycolipids and glycoproteins. This enzyme predominantly hydrolyzes ceramide trihexoside, and it can catalyze the hydrolysis of melibiose into galactose and glucose. A variety of mutations in this gene affect the synthesis, processing, and stability of this enzyme, which causes Fabry disease, a rare lysosomal storage disorder that results from a failure to catabolize alpha-D-galactosyl glycolipid moieties. [provided by RefSeq, Jul 2008]
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Purified Excitation and Emission Spectra