alpha-L-Iduronidase / Biotin /

Product Details
Supplier Biorbyt
Catalog #: orb459271 (View supplier product page)
Size 100 ug
Price $567.80
Antigen alpha-L-Iduronidase
Clone
Host Rabbit
Isotype IgG
Conjugate Biotin
Target Species Human, Mouse, Rat
Applications ELISA, IF, IHC-P, WB
Description Rabbit polyclonal antibody against MPS1 conjugated to Biotin -
About alpha-L-Iduronidase and Biotin
alpha-L-Iduronidase This gene encodes an enzyme that hydrolyzes the terminal alpha-L-iduronic acid residues of two glycosaminoglycans, dermatan sulfate and heparan sulfate. This hydrolysis is required for the lysosomal degradation of these glycosaminoglycans. Mutations in this gene that result in enzymatic deficiency lead to the autosomal recessive disease mucopolysaccharidosis type I (MPS I). [provided by RefSeq, Jul 2008]
Citations
Additional
Sources
Reviews & Ratings
Biotin Excitation and Emission Spectra