LONP1 / Biotin /

Product Details
Supplier Biorbyt
Catalog #: orb395279-Biotin (View supplier product page)
Size 100 ug
Price $547.40
Antigen LONP1
Clone
Host Mouse
Isotype IgG2a
Conjugate Biotin
Target Species Human, Mouse, Rat
Applications ICC, IF
Description Mouse monoclonal antibody to LONP1. -
About LONP1 and Biotin
LONP1 This gene encodes a mitochondrial matrix protein that belongs to the Lon family of ATP-dependent proteases. This protein mediates the selective degradation of misfolded, unassembled or oxidatively damaged polypeptides in the mitochondrial matrix. It may also have a chaperone function in the assembly of inner membrane protein complexes, and participate in the regulation of mitochondrial gene expression and maintenance of the integrity of the mitochondrial genome. Decreased expression of this gene has been noted in a patient with hereditary spastic paraplegia (PMID:18378094). Alternatively spliced transcript variants have been found for this gene. [provided by RefSeq, Feb 2013]
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Biotin Excitation and Emission Spectra