alpha Galactosidase / Biotin /

Product Details
Supplier Biorbyt
Catalog #: orb446346 (View supplier product page)
Size 100 ug
Price $567.80
Antigen alpha Galactosidase
Clone
Host Rabbit
Isotype IgG
Conjugate Biotin
Target Species Human, Mouse, Rat
Applications ELISA, IF, IHC-P, WB
Description Rabbit polyclonal antibody against Galactosidase alpha conjugated to Biotin -
About alpha Galactosidase and Biotin
alpha Galactosidase This gene encodes a homodimeric glycoprotein that hydrolyses the terminal alpha-galactosyl moieties from glycolipids and glycoproteins. This enzyme predominantly hydrolyzes ceramide trihexoside, and it can catalyze the hydrolysis of melibiose into galactose and glucose. A variety of mutations in this gene affect the synthesis, processing, and stability of this enzyme, which causes Fabry disease, a rare lysosomal storage disorder that results from a failure to catabolize alpha-D-galactosyl glycolipid moieties. [provided by RefSeq, Jul 2008]
Citations
Additional
Sources
Reviews & Ratings
Biotin Excitation and Emission Spectra