AMACR (pS504) / Unconjugated / 6F5

Product Details
Supplier HuaBio
Catalog #: EM1701-80 (View supplier product page)
Size 100 μl
Price $329.00
Antigen AMACR (pS504)
Clone 6F5
Host Mouse
Isotype IgG1
Conjugate Unconjugated
Target Species Human
Applications WB, IHC-P, FC
Description AMACR/P504S Monoclonal Antibody (EM1701-80)
About AMACR (pS504) and Purified
AMACR (pS504) This gene encodes a racemase. The encoded enzyme interconverts pristanoyl-CoA and C27-bile acylCoAs between their (R)- and (S)-stereoisomers. The conversion to the (S)-stereoisomers is necessary for degradation of these substrates by peroxisomal beta-oxidation. Encoded proteins from this locus localize to both mitochondria and peroxisomes. Mutations in this gene may be associated with adult-onset sensorimotor neuropathy, pigmentary retinopathy, and adrenomyeloneuropathy due to defects in bile acid synthesis. Alternatively spliced transcript variants have been described. Read-through transcription also exists between this gene and the upstream neighboring C1QTNF3 (C1q and tumor necrosis factor related protein 3) gene. [provided by RefSeq, Mar 2011]
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Purified Excitation and Emission Spectra