alpha Galactosidase / Biotin /
alpha Galactosidase / Biotin /
Product Details
Supplier | Bioss | |
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Catalog #: | bs-7593R-Biotin (View supplier product page) | |
Size | 100 μl | |
Price | $447.00 | |
Antigen | alpha Galactosidase | |
Clone | ||
Host | Rabbit | |
Isotype | IgG | |
Conjugate | Biotin | |
Target Species | Human, Mouse, Rat | |
Applications | WB, IHC-P |
About alpha Galactosidase and Biotin
alpha Galactosidase | This gene encodes a homodimeric glycoprotein that hydrolyses the terminal alpha-galactosyl moieties from glycolipids and glycoproteins. This enzyme predominantly hydrolyzes ceramide trihexoside, and it can catalyze the hydrolysis of melibiose into galactose and glucose. A variety of mutations in this gene affect the synthesis, processing, and stability of this enzyme, which causes Fabry disease, a rare lysosomal storage disorder that results from a failure to catabolize alpha-D-galactosyl glycolipid moieties. [provided by RefSeq, Jul 2008] |
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