alpha-L-Iduronidase / Unconjugated / 452619
alpha-L-Iduronidase / Unconjugated / 452619
Product Details
| Supplier | LifeSpan | |
|---|---|---|
| Catalog #: | LS-C125738 (View supplier product page) | |
| Size | 100 μg | |
| Price | $867.00 | |
| Antigen | alpha-L-Iduronidase | |
| Clone | 452619 | |
| Host | Mouse | |
| Isotype | IgG1 | |
| Conjugate | Unconjugated | |
| Target Species | Human | |
| Applications | ELISA, WB | |
| Description | IDUA / MPS1 Antibody (aa26-653, clone 452619) |
About alpha-L-Iduronidase and Purified
| alpha-L-Iduronidase | This gene encodes an enzyme that hydrolyzes the terminal alpha-L-iduronic acid residues of two glycosaminoglycans, dermatan sulfate and heparan sulfate. This hydrolysis is required for the lysosomal degradation of these glycosaminoglycans. Mutations in this gene that result in enzymatic deficiency lead to the autosomal recessive disease mucopolysaccharidosis type I (MPS I). [provided by RefSeq, Jul 2008] |
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Citations
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