alpha-L-Iduronidase / Unconjugated / Polyclonal

Product Details
Supplier Atlas Antibodies
Catalog #: HPA054254 (View supplier product page)
Size 100 μl
Price $439.00
Antigen alpha-L-Iduronidase
Clone Polyclonal
Host Rabbit
Isotype IgG
Conjugate Unconjugated
Target Species Human
Applications IHC
Description iduronidase, alpha-L-
About alpha-L-Iduronidase and Purified
alpha-L-Iduronidase This gene encodes an enzyme that hydrolyzes the terminal alpha-L-iduronic acid residues of two glycosaminoglycans, dermatan sulfate and heparan sulfate. This hydrolysis is required for the lysosomal degradation of these glycosaminoglycans. Mutations in this gene that result in enzymatic deficiency lead to the autosomal recessive disease mucopolysaccharidosis type I (MPS I). [provided by RefSeq, Jul 2008]
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Purified Excitation and Emission Spectra