CPS1 / Unconjugated / 8H8

Product Details
Supplier OriGene
Catalog #: AM31158PU-N (View supplier product page)
Size 50 μg
Price $380.00
Antigen CPS1
Clone 8H8
Host Mouse
Isotype IgG1
Conjugate Unconjugated
Target Species Human
Applications IHC, ELISA, WB
Description Mouse Monoclonal Anti-CPS1 Antibody, Purified
About CPS1 and Purified
CPS1 The mitochondrial enzyme encoded by this gene catalyzes synthesis of carbamoyl phosphate from ammonia and bicarbonate. This reaction is the first committed step of the urea cycle, which is important in the removal of excess urea from cells. The encoded protein may also represent a core mitochondrial nucleoid protein. Three transcript variants encoding different isoforms have been found for this gene. The shortest isoform may not be localized to the mitochondrion. Mutations in this gene have been associated with carbamoyl phosphate synthetase deficiency, susceptibility to persistent pulmonary hypertension, and susceptibility to venoocclusive disease after bone marrow transplantation.[provided by RefSeq, May 2010]
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Purified Excitation and Emission Spectra